recurrent venous thromboembolic events in a child with severe factor x deficiency

Authors

peyman eshghi pediatric congenital hematologic disorders research center, mofid children hospital, shahid beheshti university of medical sciences, tehran, iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شهید بهشتی (shahid beheshti university of medical sciences)

mohammad kajiyazdi pediatric congenital hematologic disorders research center, mofid children hospital, shahid beheshti university of medical sciences, tehran, iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شهید بهشتی (shahid beheshti university of medical sciences)

mohammad hammoud pediatric congenital hematologic disorders research center, mofid children hospital, shahid beheshti university of medical sciences, tehran, iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شهید بهشتی (shahid beheshti university of medical sciences)

abstract

congenital factor x deficiency is a rare autosomal recessive bleeding disorder that presents with variable bleeding tendency and prolonged coagulation tests, prothrombin time, and partial thromboplastin time. thromboembolic events have not been reported in patients with factor x deficiency yet. herein, we report a patient with factor x deficiency who had recurrent venous thromboembolic events.

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Journal title:
iranian journal of blood and cancer

جلد ۸، شماره ۲، صفحات ۵۶-۵۸

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